Idiopathic pulmonary fibrosis (IPF) is a relatively rare chronic, progressive lung disease with a poor prognosis. General practice nurses (GPNs) have a pivotal role in supporting patients and their families at all stages of the disease trajectory. This article aims to raise the profile of this terminal lung condition and provide nurses with an introductory understanding of the disease, the diagnostic pathway, and treatment options available for patients. As core members of the multidisciplinary team, GPNs are well-placed to provide access to other healthcare professionals and services who together can improve the lives of patients living with this condition.